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Disease Archive
Transmissible Spongiform Encephalopathy

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News
2000 2001

Outbreaks
    Chronic Wasting Disease in American Elk and Deer
Spongiform encephalopathies are chronic, degenerative diseases affecting the central nervous system. Animal forms are Bovine (BSE or "Mad Cow" disease), chronic wasting disease (CWD) in elk and deer, Transmissible (TSE) in mink and captive exotic ruminants and cats, Feline (FSE) in domestic cats and Scrapie (also a TSE) in sheep and goats. Human forms are Kuru, Creutzfeldt-Jacob (CJD), Gerstmann-Straussler-Scheinker (GSS), fatal familial insomnia (FFI) and new variant Creutzfeldt-Jacob (nvCJD). The last of these, nvCJD, is now thought to result in some consumers of beef or beef products from cattle infected with BSE. In turn, it is thought that the disease in cattle originated in their consumption of feed derived from sheep infected with Scrapie. Currently, there is some concern that CWD may be passed to humans through consumption of meat from infected deer or elk. The pathogenic agent is believed to be a deviate protein molecule called a prion. For additional information and latest research, see "Mad Cow" Disease at Continuing Concerns.